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Congenital pulmonary airway malformation

Imaging findings

Chest CT in a 28-year-old male with a hydro-pneumothorax shows a large, complex, multiloculated air-filled cystic space in the left lower lobe. Pathological analysis of the resected lobe showed ciliated bronchial-type epithelium lining the cysts, consistent with a congenital pulmonary airway malformation.

Key takeaways

Congenital pulmonary airway malformation (formerly CCAM) can remain asymptomatic until adulthood, when it may present with superinfection or spontaneous pneumothorax from cyst rupture. The presence of ciliated columnar epithelium lining the cystic walls is a key histopathological feature.

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