CTICasesAneurysmal Aortic Dissection and Rupture in Marfan Syndrome
▶ Watch on YouTube — age-restricted, cannot embed here
Imaging findings
CT angiogram in a patient with Marfan syndrome shows a complex aortic dissection of the descending aorta with a near-completely collapsed true lumen. Serial imaging shows rapid expansion of the false lumen by one centimeter over two days, followed by acute rupture, manifest on radiography as apical capping and a massive, left-sided tension hemothorax.
Key takeaways
Patients with Marfan syndrome are at extremely high risk for aggressive aortic disease, including dissection and rapid aneurysmal expansion. Aortic dimensions can change dramatically over very short intervals, and rapid enlargement of the false lumen is a warning sign of impending catastrophic rupture and exsanguination into the pleural space.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Secondary Pericardial Lymphoma from Testicular LymphomaNeoplastic
- Thoracic Endometriosis (Pulmonary Endometrioma)Other
- Diffuse Alveolar Hemorrhage in Goodpasture SyndromeAutoimmune
- Circumflex AortaCongenital
- High Origin of the Right Coronary ArteryCongenital
- Traumatic Partial Aortic TransectionTrauma
- Chronic Type B Aortic Dissection with Renal MalperfusionVascular
- Chronic Aortic Dissection with Bowel Ischemia Post-StentingVascular
See all cases from March 26, 2014 →