CTICasesPleuroparenchymal fibroelastosis
Imaging findings
Chest CT in a patient post-bone marrow transplant with chronic graft-versus-host disease shows confluent subpleural consolidation and pleural thickening predominantly in the upper lobes, along with mosaic attenuation and scattered nodularity.
Key takeaways
Pleuroparenchymal fibroelastosis (PPFE) is an increasingly recognized non-infectious pulmonary complication post-hematopoietic stem cell transplant, typically arising in the setting of chronic graft-versus-host disease. It presents with upper-lobe-predominant pleural and subpleural fibrosis and elastosis.
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