CTICasesPulmonary Capillary Hemangiomatosis
Imaging findings
Chest CT in a patient with severe pulmonary hypertension demonstrates a highly dilated and hypertrophied right ventricle, a dilated right atrium, flattening of the interventricular septum, and large, bilateral, patchy areas of ground-glass opacity without associated septal lines or findings of overt pulmonary edema.
Key takeaways
Pulmonary capillary hemangiomatosis (PCH) is a rare cause of pulmonary arterial hypertension characterized by capillary proliferation within the alveolar walls. On CT, PCH typically presents with larger patches of ground-glass opacity than the centrilobular ground-glass nodules seen with plexiform arteriopathy or other forms of pulmonary arterial hypertension.
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