Pulmonary Aplasia
Imaging findings
Chest radiograph of a premature neonate shows complete opacification of the right hemithorax with severe ipsilateral tracheal and mediastinal shift. Chest CT confirms a morphologically normal left lung with two lobes and demonstrates a blind-ending right main bronchial stump without any lung tissue or right pulmonary vasculature.
Key takeaways
Pulmonary aplasia is a congenital lung anomaly characterized by the complete absence of lung tissue and pulmonary vessels on the affected side, with only a rudimentary, blind-ending bronchus remaining. This bronchial stump distinguishes aplasia from pulmonary agenesis, although both entities are functionally identical and carry a good prognosis for normal lung function if there are no other associated life-threatening anomalies.
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