CTICasesHereditary Hemorrhagic Telangiectasia
Imaging findings
Chest CT shows multiple large pulmonary arteriovenous malformations (AVMs) with prominent feeding arteries and draining veins. Chest radiograph demonstrates tubular opacities corresponding to the AVMs.
Key takeaways
Hereditary hemorrhagic telangiectasia (HHT or Osler-Weber-Rendu disease) is an autosomal dominant disorder characterized by systemic vascular dysplasias. Pulmonary AVMs are common, can lead to right-to-left shunts, cyanosis, and paradoxical emboli, and are treated with transcatheter embolization.
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