CTICasesUnicuspid Aortic Valve and Aortic Aneurysm
Imaging findings
Cardiac MR demonstrates severe thickening and stenosis of the aortic valve with a single functioning opening, caused by fusion of the right and non-coronary leaflets, as well as the right and left leaflets. The morphology is diagnostic of a unicuspid aortic valve, which is accompanied by significant aortic regurgitation and a dilated ascending aorta representing an associated aneurysm.
Key takeaways
Unicuspid aortic valve is a rare congenital anomaly that typically presents with severe aortic valve dysfunction (stenosis or regurgitation) and ascending aortic aneurysms at a significantly younger age than bicuspid aortic valves. Detailed morphological and functional assessment can be excellently achieved with cardiac MR.
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