CTICasesLymphocytic Interstitial Pneumonia (LIP) in Sjögren Syndrome
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Imaging findings
A woman referred for evaluation of lymphangiomyomatosis (LAM), with normal kidneys and no history of tuberous sclerosis. CT revealed numerous pulmonary cysts, some displaying small vessels running through them, which is atypical for LAM. A single ground-glass nodule was also observed. Clinical evaluation showed dry eyes and positive SSA, leading to a presumptive diagnosis of Sjögren syndrome and lymphocytic interstitial pneumonia (LIP).
Key takeaways
This case illustrates lymphocytic interstitial pneumonia (LIP) associated with Sjögren syndrome, presenting with multifocal pulmonary cysts. The presence of perivascular cysts, where vessels run through or along the cyst walls, is a helpful imaging feature to differentiate LIP from LAM and other cystic lung diseases. The ground-glass nodule may represent lymphoid aggregates.
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See all cases from March 11, 2015 →