CTICasesHybrid Congenital Pulmonary Airway Malformation (CPAM) and Pulmonary Sequestration
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Imaging findings
Chest CT and 3D reconstructions demonstrate a disorganized, cystic, and multicystic parenchymal mass in the medial left lung base containing a fluid-filled bronchocoele and focal bronchial atresia. Two large, tortuous anomalous systemic arteries arise directly from the descending thoracic aorta near the level of the celiac axis to supply this malformation.
Key takeaways
Pulmonary sequestrations often coexist with other congenital lung lesions, most notably congenital pulmonary airway malformations (CPAMs), representing a "hybrid" congenital lung lesion. Identifying anomalous systemic arterial supply on CT angiography is crucial to differentiate these congenital lesions from acquired post-inflammatory neovascularization or neoplastic masses and to prevent inadvertent surgical hemorrhage.
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