CTICasesPulmonary cysts in autosomal dominant polycystic kidney disease (ADPKD)
Imaging findings
CT scan of a 52-year-old male shows ADPKD kidneys and associated extrarenal manifestations in the lungs, consisting of clustered, basally-predominant lung cysts and bronchiectasis.
Key takeaways
Lung cysts and bronchiectasis are rare, underrecognized extrarenal manifestations of ADPKD. The genetic mutations (PKD1/PKD2) are closely linked to the TSC2 gene complex, which may explain the overlap in cystic organ pathology.
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