CTICasesPlexiform neurofibromas in Neurofibromatosis type 1 (NF1)
Imaging findings
CT shows multiple large, lobulated paraspinal, mediastinal, and apical soft-tissue masses, along with neural foraminal widening and dural ectasia. A large subcutaneous mass was present on the patient's back.
Key takeaways
Plexiform neurofibromas are diagnostic of NF1 and can involve the mediastinum, spinal nerves, and subcutaneous tissues. They can cause bone remodeling (foraminal enlargement) and cord compression.
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