CTICasesPulmonary Arteriovenous Malformation with Systemic Collateral Supply
Imaging findings
Contrast-enhanced CT reveals a pulmonary arteriovenous malformation (PAVM) in the left upper lobe, fed by a pulmonary artery and draining into a pulmonary vein. Notably, systemic collaterals from both internal mammary arteries descend and penetrate the diaphragmatic surface to directly feed the malformation.
Key takeaways
While pulmonary arteriovenous malformations are typically supplied exclusively by pulmonary arteries, they can rarely recruit systemic arterial supply, particularly from the internal mammary or phrenic arteries. The presence of multiple vascular malformations combined with clinical symptoms like recurrent epistaxis strongly suggests Hereditary Hemorrhagic Telangiectasia (HHT, or Osler-Weber-Rendu syndrome).
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Duchenne Muscular Dystrophy CardiomyopathyCongenital
- Cardiac Amyloidosis with Left Atrial DominanceMetabolic
- Eosinophilic Granulomatosis with PolyangiitisAutoimmune
- Tendyne Transcatheter Mitral Valve ReplacementArtifact
- Iatrogenic Brachiocephalic Artery to Innominate Vein FistulaIatrogenic
- Unicuspid Aortic ValveCongenital
- Fontan Palliation Progression for Tricuspid AtresiaCongenital
- Tuberculosis with Empyema NecessitansInfection
See all cases from February 18, 2017 →
Related Congenital cases
- Levoatrial Cardinal Vein in Turner Syndrome
- Uncorrected D-Transposition of the Great Arteries
- Congenitally Corrected Transposition of the Great Arteries (L-TGA) with Situs Inversus
- Unilateral Pulmonary Vein Occlusion with Contralateral Pulmonary Arterial Hypertension
- Scimitar Syndrome (Hypogenetic Lung Syndrome)
- Pentalogy of Cantrell