Unicuspid Aortic Valve
Imaging findings
Cardiac CT demonstrates a severely calcified, thickened, and dysmorphic unicuspid aortic valve. The valve shows a single slit-like or teardrop-shaped functional orifice with a single commissural attachment and classic systolic doming.
Key takeaways
Unicuspid aortic valve is a rare congenital anomaly that is highly prone to early-onset calcification, stenosis, and regurgitation. It typically presents symptomatically in the third or fourth decade of life, much earlier than bicuspid aortic valves, while quadricuspid valves often remain asymptomatic and are discovered incidentally.
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