CTICasesDuchenne Muscular Dystrophy Cardiomyopathy
Imaging findings
Non-contrast chest CT shows marked, diffuse fatty atrophy of the skeletal muscles of the chest wall and shoulder girdle. The left ventricle is significantly dilated and demonstrates severe thinning of its myocardial walls with extensive, non-vascular subendocardial fatty replacement.
Key takeaways
Muscular dystrophies, such as Duchenne or Becker, frequently lead to a progressive dilated cardiomyopathy. Although early stages of the disease can demonstrate a pattern of patchy myocardial late gadolinium enhancement on cardiac MRI mimicking myocarditis (often localized to the inferolateral basal wall), advanced or burned-out cases typically present as severe global ventricular thinning and extensive fatty metaplasia.
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