CTICasesWiskott-Aldrich Syndrome Bronchiectasis
Imaging findings
Chest radiograph and CT in a young patient show severe, diffuse cystic bronchiectasis, mosaic air trapping, and dilated central pulmonary arteries with right ventricular strain/hypertrophy.
Key takeaways
Wiskott-Aldrich syndrome is a congenital immunodeficiency characterized by thrombocytopenia, eczema, and recurrent infections. Recurrent pulmonary infections lead to severe bronchiectasis and secondary pulmonary hypertension.
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