CTICases ← All cases

Isolated Main Pulmonary Artery Aneurysm from a Quadricuspid Pulmonic Valve

Imaging findings

In an asymptomatic 53-year-old woman, imaging obtained for an unrelated PE workup incidentally shows an aneurysmal main pulmonary artery, isolated to the main segment without involvement of the left or right pulmonary arteries, with mild right atrial and ventricular dilation; segmental pulmonary arteries are normal in caliber. Multiplanar CT reformats subsequently demonstrate a thickened, quadricuspid pulmonic valve.

Key takeaways

An isolated main pulmonary artery aneurysm without segmental artery enlargement or right ventricular hypertrophy to suggest pulmonary hypertension should prompt close evaluation of the pulmonic valve -- here, a quadricuspid pulmonic valve, an uncommon valve anomaly analogous to a bicuspid aortic valve, was found to be the likely underlying cause via associated post-stenotic-type dilation and wall abnormality, rather than the aneurysm being a truly idiopathic finding.

AI-assisted summary — may contain errors. Verify against the source video. Learn more

More from this webinar

See all cases from March 15, 2018 →

Related Congenital cases

Browse all Congenital cases →