CTICasesPulmonary Amyloidosis with Cystic Lung Disease in Sjögren Syndrome and MALT Lymphoma
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Imaging findings
CT of a 44-year-old woman with biliary cirrhosis, evaluated for lung transplant, showed several scattered thin-walled cystic airspaces (holes) in the lungs, some associated with dense nodular material. Biopsy confirmed amyloidosis.
Key takeaways
This patient had a history of Sjögren syndrome and MALT lymphoma, both recognized associations of pulmonary amyloidosis with cystic lung disease — a combination that can mimic or overlap with lymphocytic interstitial pneumonia (LIP), though this patient did not have LIP on biopsy.
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See all cases from June 27, 2014 →