Right Isomerism with Bilateral Tracheal Bronchi
Imaging findings
Chest CT shows right isomerism (asplenia syndrome) with bilateral tracheal bronchi (upper lobe bronchi arising directly from the trachea), bilateral morphologically right lungs, right aortic arch, retroaortic brachiocephalic vein, and abdominal situs inversus with malrotation and asplenia.
Key takeaways
Right isomerism (asplenia syndrome) is characterized by bilateral right-sidedness (bilateral trilobed lungs, asplenia). The presence of bilateral tracheal bronchi is a rare manifestation of this syndrome, which is typically associated with severe congenital heart disease.
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