Sporadic lymphangioleiomyomatosis (LAM) with retroperitoneal lymphangioma
Imaging findings
CT scan shows multiple diffuse, thin-walled cysts throughout both lungs characteristic of lymphangioleiomyomatosis (LAM), along with a large retroperitoneal cystic lymphatic malformation (lymphangioma).
Key takeaways
Lymphangioleiomyomatosis (LAM) is a rare cystic lung disease that can be sporadic or associated with tuberous sclerosis. It is frequently associated with abdominal lymphatic abnormalities such as angiomyolipomas and lymphangiomas.
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