CTICasesTetralogy of Fallot with pulmonary atresia and MAPCAs
Imaging findings
CT angiogram of a 3-week-old cyanotic newborn shows Tetralogy of Fallot with severe RV hypertrophy, VSD, and a hypoplastic/atretic RV outflow tract. Multiple large systemic collateral arteries (MAPCAs) arise from the descending aorta to supply the pulmonary parenchyma.
Key takeaways
Major aortopulmonary collateral arteries (MAPCAs) are congenital vessels that develop in the setting of severe pulmonary outflow tract obstruction (such as Tetralogy of Fallot with pulmonary atresia) to supply the lungs. Surgical management requires unifocalisation to connect collaterals to a reconstructed pulmonary trunk.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Chest wall chondrosarcomaNeoplastic
- Transient phrenic nerve palsy secondary to brachial plexus blockIatrogenic
- Primary endobronchial diffuse large B-cell lymphomaNeoplastic
- Primary pulmonary MALT lymphomaNeoplastic
- Pulmonary vascular telangiectasias in sickle cell diseaseCongenital
- Large mediastinal thymic cystCongenital
- Mature mediastinal teratomaNeoplastic
- Disseminated extraosseous multiple myelomaNeoplastic
See all cases from September 26, 2019 →
Related Congenital cases
- Superior sinus venosus ASD and PAPVR
- Pulmonary cysts in autosomal dominant polycystic kidney disease (ADPKD)
- Common origin of the subclavian arteries simulating a paratracheal mass
- Multiple visceral aneurysms in Menkes syndrome
- Osteosclerosis and myocardial fat in tuberous sclerosis
- Hypoplastic left heart syndrome with coronary-left atrial fistula