CTICasesErdheim-Chester Syndrome
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Imaging findings
Infiltrative soft tissue drapes around the mediastinal vessels, heart, and throughout the abdomen in a perirenal distribution. The patient also exhibits characteristic distal osteosclerosis.
Key takeaways
A rare systemic histiocytosis characterized by the "coated" appearance of mediastinal structures and vessels, with distal osteosclerosis serving as a key diagnostic clue; prognosis is poorer with cardiac or pulmonary involvement.
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