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Eosinophilic Granulomatosis with Polyangiitis

Imaging findings

Radiographs and CT show multifocal, patchy, non-segmental lung consolidation and ground-glass opacities, demonstrating peripheral sparing and simulating organizing pneumonia or chronic eosinophilic pneumonia.

Key takeaways

Eosinophilic granulomatosis with polyangiitis (EGPA, formerly Churg-Strauss syndrome) typically presents with asthma, chronic sinusitis, peripheral blood eosinophilia, and p-ANCA positivity. Pulmonary manifestations include transient, non-segmental areas of consolidation or ground-glass opacity that mimic eosinophilic pneumonia and characteristically show a dramatic response to corticosteroid therapy.

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