CTICasesLymphoid interstitial pneumonia (LIP) in Sjögren's syndrome
Imaging findings
Serial CT scans over 11 years show progressive enlargement and confluence of multiple thin-walled, perivascular cysts in a basally predominant distribution, complicated by a spontaneous pneumothorax.
Key takeaways
LIP is a benign lymphoproliferative disorder strongly associated with Sjögren's syndrome. The classic CT finding is thin-walled perivascular cysts that can enlarge slowly over decades and cause spontaneous pneumothorax.
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