CTICasesEffusive-constrictive pericarditis in sickle cell disease
Imaging findings
Echocardiography shows a massive, highly septated pericardial effusion with atrial chamber collapse consistent with cardiac tamponade. Follow-up cardiac MRI after drainage of 2 liters of fluid shows a residual effusion, marked pericardial thickening with septations, and tubular ventricles.
Key takeaways
Sickle cell disease can be associated with severe, chronic, or recurrent pericarditis. In cases of large, septated effusions, effusive-constrictive physiology may remain even after fluid drainage due to the underlying visceral pericardial thickening and inflammation.
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