Unrepaired sinus venosus ASD and PAPVR in a heart transplant recipient
Imaging findings
CT scan of a heart transplant recipient demonstrates anomalous pulmonary venous drainage of the right superior pulmonary vein directly into the superior vena cava (PAPVR), and a failing sinus venosus ASD patch. These anomalies involved the native recipient structures and were missed during transplantation.
Key takeaways
During orthotopic heart transplantation, a portion of the native recipient's posterior left atrium and SVC are typically preserved. Any pre-existing anomalous pulmonary venous return or sinus venosus ASDs in these segments must be identified and repaired, or they will cause a persistent postoperative left-to-right shunt.
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