CTICasesSoft Tissue Calcinosis and Diaphragmatic Hypertrophy in Scleroderma with Myositis
Imaging findings
Extensive and progressive soft tissue calcinosis is evident throughout the chest and abdominal wall, appearing much worse than on prior studies. The crura of the diaphragm are grossly hypertrophied, a finding that has dramatically worsened over four years.
Key takeaways
This striking case illustrates severe, progressive soft tissue calcinosis in scleroderma with a myositis component, leading to dramatic restriction of chest wall and abdominal movement. The resulting increased inspiratory effort against a rigid abdominal wall has caused compensatory hypertrophy of the diaphragmatic crura, a physiological adaptation akin to that seen in weightlifters performing forced breathing maneuvers.
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