Pleuroparenchymal fibroelastosis
Imaging findings
Chest radiograph and CT show bilateral upper lung volume loss, marked apical pleural thickening, and subpleural reticulation, associated with biopsy findings of both pleuroparenchymal fibroelastosis and chronic hypersensitivity pneumonitis.
Key takeaways
Pleuroparenchymal fibroelastosis is a rare interstitial lung disease characterized by pleural and subpleural parenchymal fibroelastosis, predominantly affecting the upper lobes. It can be idiopathic or secondary to conditions like chronic hypersensitivity pneumonitis.
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