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Arrhythmogenic Right Ventricular Dysplasia

Arrhythmogenic Right Ventricular Dysplasia▶ Watch on YouTube — age-restricted, cannot embed here

Imaging findings

Cardiac MRI demonstrates severe dilation of the right ventricle, right ventricular ejection fraction under 40 percent, and dyskinetic, akinetic, or aneurysmal outpouchings along the anterior right ventricular free wall, with a structurally normal right atrium and tricuspid valve.

Key takeaways

Arrhythmogenic right ventricular dysplasia is a genetic desmosomal cardiomyopathy that presents with ventricular arrhythmias, right heart failure, and sudden cardiac death. Cardiac MRI plays a key role in the task force diagnostic criteria, looking for right ventricular dilation, global dysfunction, and regional wall motion abnormalities such as akinesis or dyskinesis.

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