Arrhythmogenic Right Ventricular Dysplasia
▶ Watch on YouTube — age-restricted, cannot embed here
Imaging findings
Cardiac MRI demonstrates severe dilation of the right ventricle, right ventricular ejection fraction under 40 percent, and dyskinetic, akinetic, or aneurysmal outpouchings along the anterior right ventricular free wall, with a structurally normal right atrium and tricuspid valve.
Key takeaways
Arrhythmogenic right ventricular dysplasia is a genetic desmosomal cardiomyopathy that presents with ventricular arrhythmias, right heart failure, and sudden cardiac death. Cardiac MRI plays a key role in the task force diagnostic criteria, looking for right ventricular dilation, global dysfunction, and regional wall motion abnormalities such as akinesis or dyskinesis.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Spontaneous Pneumomediastinum and Pneumoretroperitoneum due to Macklin PhenomenonOther
- Thoracic Spine Discitis-Osteomyelitis and Paraspinal Abscess due to Disseminated Mycobacterium avium complexInfection
- Right Ventricular Perforation and Pericardial Contrast InjectionIatrogenic
- Esophagopericardial FistulaOther
- Congenital Hypoplasia of the Right Upper LobeCongenital
- Goodpasture Syndrome (Anti-GBM Disease)Autoimmune
- Behçet Syndrome with Multiple Pulmonary Artery AneurysmsAutoimmune
- Left Ventricular Pseudoaneurysm post-TAVRIatrogenic
See all cases from July 7, 2014 →