Eosinophilic Granulomatosis with Polyangiitis
Imaging findings
CT chest shows diffuse, patchy, peripheral ground-glass opacities, septal thickening (crazy paving), and areas of subpleural consolidation. Follow-up imaging shows rapid, complete clearing after initiating corticosteroid therapy.
Key takeaways
Eosinophilic granulomatosis with polyangiitis (EGPA, formerly Churg-Strauss syndrome) is a necrotizing vasculitis characterized by eosinophilia and asthma. Thoracic manifestations include transient, migratory ground-glass opacities or peripheral consolidations (representing eosinophilic pneumonia) that are highly steroid-responsive.
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