Pulmonary Artery Aneurysms in Behçet Disease
[...]. Pulmonary Artery Aneurysms in Behçet Disease. CTICases. Published September 24, 2021. https://cticases.com/c/vyawd
Imaging findings
CT angiography shows multiple, large, bilateral pulmonary artery aneurysms, with focal areas of occlusion and pulmonary infarction. Coils from prior aneurysm embolization are noted, showing a fistulous tract communication to an adjacent bronchus.
Key takeaways
Behçet disease is a systemic vasculitis that uniquely causes pulmonary artery aneurysms. Transcatheter embolization is the primary treatment, but the coil pack can erode the adjacent bronchial wall, creating a bronchoarterial fistula and predisposing patients to massive hemoptysis.
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