CTICasesCongenital Coronary-Cameral Fistula in Fontan Circulation
Imaging findings
CT angiography and MRI in a patient with tricuspid atresia, hypoplastic right ventricle, and lateral tunnel Fontan repair demonstrate a dilated left ventricle. There is a congenital coronary-cameral fistula connecting the obtuse marginal artery to the hypoplastic right ventricle apex, and a dilated coronary sinus communicating with the left atrium.
Key takeaways
Coronary-cameral fistulas are rare congenital vascular anomalies connecting a coronary artery to a cardiac chamber. In patients with Fontan circulation (such as for tricuspid atresia), shunting of blood into the hypoplastic right ventricle can be exacerbated by elevated left atrial and pulmonary pressures, requiring closure during valve surgery.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Erdheim-Chester DiseaseNeoplastic
- Pulmonary Tumor Thrombotic MicroangiopathyNeoplastic
- Systemic AL AmyloidosisMetabolic
- Nocardia nova InfectionInfection
- Recanalized Pulmonary Arteriovenous MalformationCongenital
- Sulfasalazine-Induced Organizing PneumoniaExposure
- Multifocal Synchronous Lung AdenocarcinomasNeoplastic
- Right Middle Lobe Collapse from Sarcoid LymphadenopathyInflammatory
See all cases from December 17, 2019 →