CTICasesMounier-Kuhn syndrome (tracheobronchomegaly)
Imaging findings
CT chest shows marked dilatation of the trachea and main bronchi with characteristic scalloping and corrugation of the airway margins between cartilaginous rings, along with chronic basilar consolidation and bronchiectasis.
Key takeaways
Mounier-Kuhn syndrome is a rare congenital disorder characterized by atrophy of the elastic fibers and smooth muscle within the trachea and main bronchi. This leads to tracheobronchomegaly and tracheal diverticulosis (corrugation pattern), predisposing to recurrent infections and aspiration.
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