CTICasesAortic and bone involvement in Erdheim-Chester disease
Imaging findings
CT demonstrates diffuse wall thickening and calcification of the thoracic and abdominal aorta in a 30-year-old female. Scout views and radiographs show characteristic, symmetric cortical osteosclerosis of the long bones.
Key takeaways
Erdheim-Chester disease is a non-Langerhans cell histiocytosis that can cause circumferential infiltration of the aortic wall ('coated aorta'). Finding symmetric metadiaphyseal sclerosis of the long bones on plain films is key to differentiating it from other causes of aortitis.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Severe achalasia (megaesophagus)Other
- Mounier-Kuhn syndrome (tracheobronchomegaly)Congenital
- Aortitis in systemic sarcoidosisAutoimmune
- Miliary metastases from EGFR-mutant lung adenocarcinomaNeoplastic
- Iatrogenic esophageal perforation post-mediastinoscopyIatrogenic
- Aortic valve thrombus causing myocardial infarction in protein S deficiencyVascular
- Lobar torsion secondary to lung adenocarcinomaNeoplastic
- Undifferentiated pleomorphic sarcoma of the mediastinumNeoplastic
See all cases from July 18, 2019 →