CTICasesMatong Disease (Diffuse Symmetric Lipomatosis)
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Imaging findings
The patient's chest wall showed extensive, swirling, somewhat discrete, partially encapsulated fatty masses (lipomas), some with calcifications. This appearance was described as resembling a 'buffalo hump'. The fat was noted to be brown fat.
Key takeaways
Matong disease, also known as diffuse symmetric lipomatosis or Lenois-Benad disease, is a rare condition characterized by the symmetrical accumulation of encapsulated lipomas, often involving the neck, upper back, and shoulders, but can extend to the chest wall. While sometimes associated with alcoholism, it can occur independently. The adipose tissue is believed to be brown fat.
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