CTICases ← All cases

Pulmonary Agenesis and Persistent Left Superior Vena Cava with Aberrant Drainage

Pulmonary Agenesis and Persistent Left Superior Vena Cava with Aberrant Drainage▶ Watch on YouTube — age-restricted, cannot embed here

Imaging findings

Unilateral pulmonary agenesis (absent left pulmonary artery, with the left lung supplied by bronchial collaterals) in a patient with repaired congenital heart disease (RV to conduit, VSD patch repair). A persistent left superior vena cava (PLSVC) was observed with an abnormal course, descending lateral to the aortic arch, then coursing medially to drain into the right atrium, rather than into the coronary sinus or anterior to the left pulmonary artery.

Key takeaways

Persistent left superior vena cava can present with anomalous courses, especially in conjunction with other congenital heart defects like pulmonary agenesis. The aberrant course of the PLSVC in this case was likely influenced by the absence of the left pulmonary artery, highlighting embryological variations.

AI-assisted summary — may contain errors. Verify against the source video. Learn more

More from this webinar

See all cases from October 24, 2014 →

Related Congenital cases

Browse all Congenital cases →