CTICases ← All cases

CVID with Granulomatous-Lymphocytic Interstitial Lung Disease

Imaging findings

CT chest in a patient with common variable immunodeficiency (CVID) shows diffuse splenomegaly, mediastinal lymphadenopathy, and multiple faint ground-glass nodules forming a 'fairy ring' sign (halo/reversed halo of fine micronodules). Biopsy confirmed GLILD.

Key takeaways

Granulomatous-lymphocytic interstitial lung disease (GLILD) is a rare, non-infectious pulmonary complication of CVID. It is characterized by lymphoid hyperplasia and non-caseating granulomas, mimicking sarcoidosis. CT signs such as the 'fairy ring' of fine nodules can help differentiate it from lymphoma or infection.

AI-assisted summary — may contain errors. Verify against the source video. Learn more

More from this webinar

See all cases from April 30, 2020 →

Related Autoimmune cases

Browse all Autoimmune cases →