CVID with Granulomatous-Lymphocytic Interstitial Lung Disease
Imaging findings
CT chest in a patient with common variable immunodeficiency (CVID) shows diffuse splenomegaly, mediastinal lymphadenopathy, and multiple faint ground-glass nodules forming a 'fairy ring' sign (halo/reversed halo of fine micronodules). Biopsy confirmed GLILD.
Key takeaways
Granulomatous-lymphocytic interstitial lung disease (GLILD) is a rare, non-infectious pulmonary complication of CVID. It is characterized by lymphoid hyperplasia and non-caseating granulomas, mimicking sarcoidosis. CT signs such as the 'fairy ring' of fine nodules can help differentiate it from lymphoma or infection.
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