CTICasesMelorheostosis with Tracheobronchial Involvement
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Imaging findings
The patient presented with a large, slowly growing blastic lesion arising from and continuous with the cortex of the right clavicle, radiating outward, consistent with melorheostosis. Unilaterally, on the right side of the trachea and main bronchi (right upper and middle lobe bronchi), there were several nodules and encasement by abnormal bone-like tissue, resembling the 'candle wax dripping' appearance seen in the clavicle. Similar dense bone was noted in the costal cartilages.
Key takeaways
Melorheostosis is a rare sclerosing bone dysplasia characterized by hyperostosis that resembles 'flowing candle wax' on imaging. This case highlights an exceptionally rare presentation of melorheostosis-like changes affecting not only bone but also cartilage-rich structures like the trachea and main bronchi, primarily in a unilateral distribution. This raises questions about the scope of tissues affected by this condition.
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