Extramedullary Hematopoiesis in Thalassemia
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Imaging findings
Frontal chest radiograph demonstrates multiple bilateral extra-pleural opacities, some exhibiting an incomplete border sign, located adjacent to the ribs. CT shows substantial involvement of the bone marrow in the rib cage, producing para-rib extra-pleural opacities of hematopoietic tissue, and paraspinal opacities, along with abnormal bone marrow and trabeculation.
Key takeaways
Extramedullary hematopoiesis commonly presents with para-rib extra-pleural masses, particularly in patients with chronic hemolytic anemias like thalassemia. Imaging findings also include abnormal bone marrow expansion and altered trabeculation in bones.
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