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Extramedullary Hematopoiesis in Thalassemia

Extramedullary Hematopoiesis in Thalassemia▶ Watch on YouTube — age-restricted, cannot embed here

Imaging findings

Frontal chest radiograph demonstrates multiple bilateral extra-pleural opacities, some exhibiting an incomplete border sign, located adjacent to the ribs. CT shows substantial involvement of the bone marrow in the rib cage, producing para-rib extra-pleural opacities of hematopoietic tissue, and paraspinal opacities, along with abnormal bone marrow and trabeculation.

Key takeaways

Extramedullary hematopoiesis commonly presents with para-rib extra-pleural masses, particularly in patients with chronic hemolytic anemias like thalassemia. Imaging findings also include abnormal bone marrow expansion and altered trabeculation in bones.

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