CTICasesIgG4-Related Sclerosing Disease mimicking Vasculitis
Imaging findings
Chest CT shows a soft tissue mass in the mediastinum causing focal narrowing and compression of the left pulmonary artery. Biopsy of the tissue confirmed IgG4-related sclerosing disease, showing dense lymphoplasmacytic infiltration and sclerosis.
Key takeaways
IgG4-related disease is a systemic fibro-inflammatory condition that can mimic primary large-vessel vasculitis or fibrosing mediastinitis. It can form a focal mediastinal mass that directly invades or compresses the pulmonary arteries and aorta.
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